Síndrome de Susac: reporte de caso

Sara Arias; Mariana Gómez; Luis Gustavo Celis

doi:10.22490/24629448.1720

Susac Syndrome: Case Report

Síndrome de Susac: reporte de caso

Published 2015-12-30

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Vol. 13 No. 24 (2015)

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Reporte de Caso

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Arias, S., Gómez, M., & Celis, L. G. (2015). Susac Syndrome: Case Report. NOVA, 13(24), 101-106. https://doi.org/10.22490/24629448.1720

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https://doi.org/10.22490/24629448.1720

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NOVA by http://www.unicolmayor.edu.co/publicaciones/index.php/nova is distributed under a license creative commons non comertial-atribution-withoutderive 4.0 international.

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Sara Arias

Universidad de La Sabana

Mariana Gómez

Universidad de La Sabana

Luis Gustavo Celis

Universidad de La Sabana

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Acute encephalomyelitis

Alopsiquia

Ataxia

Devic’s disease

Hyporeflexia

Multiple sclerosis

Susac’s syndrome

Objective. To describe the case of a 23 year-old female patient disoriented in space and time, with an oppressive left-sided temporal headache, associated with ataxia, and bradypsychia. Methods. A possible multiple sclerosis associated to the clinical and paraclinical tests was suspected at the beginning. An acute disseminated encephalomyelitis was suspected and treated with methylprednisolone pulses and patient was discharged. Within a month, she required again due to exacerbation of neurological symptoms given by a loss of strength in upper and lower limbs, dysarthria, wetting, and drowsiness. Devic’s disease was diagnosed initially. Because response to corticosteroids was not the expected, it was decided to treat with plasmapheresis; in addition, new tests were requested to rule out the suspected disease. Results. Treatment was focused on a possible diagnosis of Susac’s syndrome with an arteriography retinal test and potential auditory evoked.

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